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| PATHWAY_NAME | REACTOME_ID | KEGG_ID | DRUG_NAME | PUBCHEM_CID | Datasource |
|---|---|---|---|---|---|
| Primary Hyperoxaluria Type I | R-HSA-5601905 | 0 | Biotin | 135398737 | smpdb |
| Leigh Syndrome | R-HSA-2206302 | 0 | Biotin | 135398737 | smpdb |
| Propanoate Metabolism | R-HSA-1430728 | map00640 | Biotin | 135398737 | smpdb |
| Methylmalonic Aciduria | R-HSA-3359471 | 0 | Biotin | 135398737 | smpdb |
| Methylmalonic Aciduria Due to Cobalamin-Related Disorders | 0 | 0 | Biotin | 135398737 | smpdb |
| Glycogenosis, Type IC | R-ALL-9605649 | 0 | Biotin | 135398737 | smpdb |
| Propionic Acidemia | R-ALL-429737 | 0 | Biotin | 135398737 | smpdb |
| Mitochondrial Complex II Deficiency | R-HSA-5602680 | 0 | Biotin | 135398737 | smpdb |
| 3-Methylglutaconic Aciduria Type IV | R-HSA-215993 | 0 | Biotin | 135398737 | smpdb |
| Primary Hyperoxaluria II, PH2 | R-HSA-5601905 | 0 | Biotin | 135398737 | smpdb |
| Pyruvate Metabolism | R-HSA-70268 | map00620 | Biotin | 135398737 | smpdb |
| Phosphoenolpyruvate Carboxykinase Deficiency 1 | R-HSA-560472 | 0 | Biotin | 135398737 | smpdb |
| 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I | 0 | 0 | Biotin | 135398737 | smpdb |
| Homocarnosinosis | 0 | 0 | Biotin | 135398737 | smpdb |
| Triosephosphate Isomerase Deficiency | R-HSA-2465932 | 0 | Biotin | 135398737 | smpdb |
| Isobutyryl-CoA Dehydrogenase Deficiency | R-ALL-70851 | 0 | Biotin | 135398737 | smpdb |
| LPS and Citrate Signaling and Inflammation | R-ALL-166005 | 0 | Biotin | 135398737 | smpdb |
| Lactic Acidemia | R-HSA-70268 | 0 | Biotin | 135398737 | smpdb |
| Ammonia Recycling | R-HSA-1222583 | 0 | Biotin | 135398737 | smpdb |
| Isovaleric Aciduria | R-ALL-9737163 | 0 | Biotin | 135398737 | smpdb |