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Drug-Pathway
DRUGs and PATHWAYs
PATHWAY_NAME REACTOME_ID KEGG_ID DRUG_NAME PUBCHEM_CID Datasource
Valine, Leucine, and Isoleucine Degradation R-HSA-1442490 0 Pyridoxal 4806 smpdb
Isobutyryl-CoA Dehydrogenase Deficiency R-ALL-70851 0 Pyridoxal 4806 smpdb
Methylmalonate Semialdehyde Dehydrogenase Deficiency 0 0 Pyridoxal 4806 smpdb
Vitamin B6 Metabolism R-HSA-6806664 map00750 Pyridoxal 4806 smpdb
3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency R-HSA-5602680 0 Pyridoxal 4806 smpdb
2-Methyl-3-hydroxybutryl-CoA Dehydrogenase Deficiency 0 0 Pyridoxal 4806 smpdb
Hypophosphatasia 0 0 Pyridoxal 4806 smpdb
3-Methylglutaconic Aciduria Type I R-ALL-9605649 0 Pyridoxal 4806 smpdb
beta-Ketothiolase Deficiency R-HSA-5602680 0 Pyridoxal 4806 smpdb
3-Hydroxyisobutyric Acid Dehydrogenase Deficiency R-HSA-9027561 0 Pyridoxal 4806 smpdb
3-Hydroxyisobutyric Aciduria R-HSA-70885 0 Pyridoxal 4806 smpdb
3-Methylcrotonyl-CoA Carboxylase Deficiency Type I 0 0 Pyridoxal 4806 smpdb
Isovaleric Aciduria R-ALL-9737163 0 Pyridoxal 4806 smpdb
3-Methylglutaconic Aciduria Type IV R-HSA-215993 0 Pyridoxal 4806 smpdb
Hyperornithinemia-Hyperammonemia-Homocitrullinuria [HHH-syndrome] 0 0 Creatine 586 smpdb
Glycine and Serine Metabolism R-HSA-389661 0 Creatine 586 smpdb
Non-Ketotic Hyperglycinemia R-HSA-6783984 0 Creatine 586 smpdb
Ornithine Aminotransferase Deficiency R-HSA-5602680 0 Creatine 586 smpdb
Guanidinoacetate Methyltransferase Deficiency R-HSA-5602680 0 Creatine 586 smpdb
Dihydropyrimidine Dehydrogenase Deficiency R-HSA-9027561 0 Creatine 586 smpdb