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Drug-Pathway
DRUGs and PATHWAYs
PATHWAY_NAME REACTOME_ID KEGG_ID DRUG_NAME PUBCHEM_CID Datasource
Isovaleric Acidemia R-ALL-9737163 0 Oxoglutaric acid 108150 smpdb
Propanoate Metabolism R-HSA-1430728 map00640 Oxoglutaric acid 108150 smpdb
3-Methylglutaconic Aciduria Type IV R-HSA-215993 0 Oxoglutaric acid 108150 smpdb
3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency R-HSA-5602680 0 Oxoglutaric acid 108150 smpdb
2-Ketoglutarate Dehydrogenase Complex Deficiency R-HSA-9027561 0 Oxoglutaric acid 108150 smpdb
Citric Acid Cycle R-HSA-71403 0 Oxoglutaric acid 108150 smpdb
Canavan Disease R-HSA-1643685 0 Oxoglutaric acid 108150 smpdb
Cystinosis, Ocular Nonnephropathic R-HSA-5619054 0 Oxoglutaric acid 108150 smpdb
Fumarase Deficiency R-HSA-5602680 0 Oxoglutaric acid 108150 smpdb
Dimethylglycine Dehydrogenase Deficiency R-HSA-9027561 0 Oxoglutaric acid 108150 smpdb
Phenylketonuria R-HSA-2160456 0 Oxoglutaric acid 108150 smpdb
Creatine Deficiency, Guanidinoacetate Methyltransferase Deficiency 0 0 Oxoglutaric acid 108150 smpdb
Methylmalonate Semialdehyde Dehydrogenase Deficiency 0 0 Oxoglutaric acid 108150 smpdb
Malonic Aciduria R-ALL-909783 0 Oxoglutaric acid 108150 smpdb
Hyperinsulinism-Hyperammonemia Syndrome R-HSA-2206302 0 Oxoglutaric acid 108150 smpdb
Ornithine Transcarbamylase Deficiency R-HSA-5602680 0 Oxoglutaric acid 108150 smpdb
beta-Mercaptolactate-Cysteine Disulfiduria R-HSA-1614558 0 Oxoglutaric acid 108150 smpdb
Succinate Signalling R-HSA-187687 0 Oxoglutaric acid 108150 smpdb
Glycogenosis, Type IA. Von Gierke Disease R-HSA-1643685 0 Oxoglutaric acid 108150 smpdb
Prolidase Deficiency R-HSA-5602680 0 Oxoglutaric acid 108150 smpdb