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Drug-Pathway
DRUGs and PATHWAYs
PATHWAY_NAME REACTOME_ID KEGG_ID DRUG_NAME PUBCHEM_CID Datasource
Vitamin K Metabolism R-HSA-6806664 0 Methylmalonic acid 443874 smpdb
Maple Syrup Urine Disease R-HSA-1643685 0 Methylmalonic acid 443874 smpdb
3-Methylglutaconic Aciduria Type IV R-HSA-215993 0 Methylmalonic acid 443874 smpdb
3-Hydroxyisobutyric Acid Dehydrogenase Deficiency R-HSA-9027561 0 Methylmalonic acid 443874 smpdb
3-Hydroxyisobutyric Aciduria R-HSA-70885 0 Methylmalonic acid 443874 smpdb
3-Methylglutaconic Aciduria Type III R-HSA-2127436 0 Methylmalonic acid 443874 smpdb
Isobutyryl-CoA Dehydrogenase Deficiency R-ALL-70851 0 Methylmalonic acid 443874 smpdb
Methionine Metabolism R-HSA-5676912 0 L-Homoserine 1549144 smpdb
Methylenetetrahydrofolate Reductase Deficiency R-HSA-9024779 0 L-Homoserine 1549144 smpdb
Glycine N-Methyltransferase Deficiency R-HSA-5602680 0 L-Homoserine 1549144 smpdb
S-Adenosylhomocysteine Hydrolase Deficiency R-HSA-8939794 0 L-Homoserine 1549144 smpdb
Cystathionine beta-Synthase Deficiency R-ALL-936600 0 L-Homoserine 1549144 smpdb
Homocystinuria-Megaloblastic Anemia Due to Defect in Cobalamin Metabolism, cblG Complementation Type 0 0 L-Homoserine 1549144 smpdb
Methionine Adenosyltransferase Deficiency R-HSA-5676912 0 L-Homoserine 1549144 smpdb
Hypermethioninemia R-HSA-5578997 0 L-Homoserine 1549144 smpdb
Hyperlysinemia II or Saccharopinuria R-ALL-1973971 0 Saccharopine 33032 smpdb
Pyridoxine Dependency with Seizures R-ALL-965053 0 Saccharopine 33032 smpdb
Hyperlysinemia I, Familial R-HSA-6809602 0 Saccharopine 33032 smpdb
Lysine Degradation R-HSA-71064 map00310 Saccharopine 33032 smpdb
2-Aminoadipic 2-Oxoadipic Aciduria R-ALL-113577 0 Saccharopine 33032 smpdb